4-Methylumbelliferyl-α-L-Iduronicacidcyclohexylammoniumsalt
4-Methylumbelliferyl-α-L-iduronide.
4-MU-α-L-IdoA•CHX
MOLECULARBIOLOGYGRADE
C16H16O9·C6H13N
MW:451.48g/mol
Off-whitepowder
Fluorogenicsolubleenzymesubstrateforα-L-iduronidase.α-L-iduronidaseisdeficientinthegeneticdisorderMucopolysaccharidosistypeI,alsocalledHurlersyndrome.DiagnosisofHurlersyndromeinvolvesenzymaticassayofα-L-iduronidaseactivityusingthefluorogenicenzymesubstrate4-Methylumbelliferyl-α-L-iduronide.
Storage/Handling:Storeat-15°Cinadark,dryplace.